Obesity-induced CerS6-dependent C 16: 0 ceramide production promotes weight gain and glucose intolerance SM Turpin, HT Nicholls, DM Willmes, A Mourier, S Brodesser, ... Cell metabolism 20 (4), 678-686, 2014 | 370 | 2014 |
Germline mtDNA mutations aggravate ageing and can impair brain development JM Ross, JB Stewart, E Hagström, S Brené, A Mourier, G Coppotelli, ... Nature 501 (7467), 412, 2013 | 230 | 2013 |
Adipose-specific deletion of TFAM increases mitochondrial oxidation and protects mice against obesity and insulin resistance C Vernochet, A Mourier, O Bezy, Y Macotela, J Boucher, MJ Rardin, D An, ... Cell metabolism 16 (6), 765-776, 2012 | 166 | 2012 |
MICOS coordinates with respiratory complexes and lipids to establish mitochondrial inner membrane architecture JR Friedman, A Mourier, J Yamada, JM McCaffery, J Nunnari Elife 4, e07739, 2015 | 145 | 2015 |
Mitofusin 2 is required to maintain mitochondrial coenzyme Q levels A Mourier, E Motori, T Brandt, M Lagouge, I Atanassov, A Galinier, ... J Cell Biol 208 (4), 429-442, 2015 | 138 | 2015 |
Mitofusin 2 is necessary for striatal axonal projections of midbrain dopamine neurons S Lee, FH Sterky, A Mourier, M Terzioglu, S Cullheim, L Olson, ... Human molecular genetics 21 (22), 4827-4835, 2012 | 126 | 2012 |
Variation in germline mtDNA heteroplasmy is determined prenatally but modified during subsequent transmission C Freyer, LM Cree, A Mourier, JB Stewart, C Koolmeister, D Milenkovic, ... Nature genetics 44 (11), 1282-1285, 2012 | 117 | 2012 |
Adipose tissue mitochondrial dysfunction triggers a lipodystrophic syndrome with insulin resistance, hepatosteatosis, and cardiovascular complications C Vernochet, F Damilano, A Mourier, O Bezy, MA Mori, G Smyth, ... The FASEB Journal 28 (10), 4408-4419, 2014 | 99 | 2014 |
MTERF1 binds mtDNA to prevent transcriptional interference at the light-strand promoter but is dispensable for rRNA gene transcription regulation M Terzioglu, B Ruzzenente, J Harmel, A Mourier, E Jemt, MD López, ... Cell metabolism 17 (4), 618-626, 2013 | 98 | 2013 |
Loss of LRPPRC causes ATP synthase deficiency A Mourier, B Ruzzenente, T Brandt, W Kühlbrandt, NG Larsson Human molecular genetics 23 (10), 2580-2592, 2014 | 95 | 2014 |
MTERF3 regulates mitochondrial ribosome biogenesis in invertebrates and mammals A Wredenberg, M Lagouge, A Bratic, MD Metodiev, H Spåhr, A Mourier, ... PLoS genetics 9 (1), e1003178, 2013 | 92 | 2013 |
The respiratory chain supercomplex organization is independent of COX7a2l isoforms A Mourier, S Matic, B Ruzzenente, NG Larsson, D Milenkovic Cell metabolism 20 (6), 1069-1075, 2014 | 79 | 2014 |
Transcriptomic and proteomic landscape of mitochondrial dysfunction reveals secondary coenzyme Q deficiency in mammals I Kühl, M Miranda, I Atanassov, I Kuznetsova, Y Hinze, A Mourier, ... Elife 6, e30952, 2017 | 68 | 2017 |
Transcriptomic and proteomic landscape of mitochondrial dysfunction reveals secondary coenzyme Q deficiency in mammals I Kühl, M Miranda, I Atanassov, I Kuznetsova, Y Hinze, A Mourier, ... eLife 6, 2017 | 68 | 2017 |
Hierarchical RNA processing is required for mitochondrial ribosome assembly O Rackham, JD Busch, S Matic, SJ Siira, I Kuznetsova, I Atanassov, ... Cell reports 16 (7), 1874-1890, 2016 | 68 | 2016 |
Rescue of primary ubiquinone deficiency due to a novel COQ7 defect using 2,4–dihydroxybensoic acid C Freyer, H Stranneheim, K Naess, A Mourier, A Felser, C Maffezzini, ... Journal of medical genetics 52 (11), 779-783, 2015 | 62 | 2015 |
A phenotype-driven approach to generate mouse models with pathogenic mtDNA mutations causing mitochondrial disease JHK Kauppila, HL Baines, A Bratic, ML Simard, C Freyer, A Mourier, ... Cell reports 16 (11), 2980-2990, 2016 | 61 | 2016 |
COX7A2L Is a Mitochondrial Complex III Binding Protein that Stabilizes the III 2+ IV Supercomplex without Affecting Respirasome Formation R Pérez-Pérez, T Lobo-Jarne, D Milenkovic, A Mourier, A Bratic, ... Cell reports 16 (9), 2387-2398, 2016 | 60 | 2016 |
Loss of UCP2 attenuates mitochondrial dysfunction without altering ROS production and uncoupling activity A Kukat, SA Dogan, D Edgar, A Mourier, C Jacoby, P Maiti, J Mauer, ... PLoS genetics 10 (6), e1004385, 2014 | 58 | 2014 |
POLRMT regulates the switch between replication primer formation and gene expression of mammalian mtDNA I Kühl, M Miranda, V Posse, D Milenkovic, A Mourier, SJ Siira, ... Science advances 2 (8), e1600963, 2016 | 54 | 2016 |